NA03755
DNA from Fibroblast
Description:
DYSTROPHIA MYOTONICA 1; DM1
Repository
|
NIGMS Human Genetic Cell Repository
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Subcollection |
Heritable Diseases |
Quantity |
0.050mg |
Quantitation Method |
Please see our FAQ |
Sample Source
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DNA from Fibroblast
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Race
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White
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Family Member
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1
|
Relation to Proband
|
proband
|
Confirmation
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Molecular characterization - other
|
Species
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Homo sapiens
|
Common Name
|
Human
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Remarks
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|
Remarks |
Typical phenotype; mother, 2 brothers and a sister also affected; see GM03756 Lymphoid; characterization of lymphoblast DNA showed expansion of CTG repeat is <1.5 kb detectable by Southern analysis corresponding to up to 500 CTG repeats; heterozygous for a C-to-T substitution at nucleotide 677 that converts an alanine to a valine residue in the methylenetetrahydrofolate reductase (MTHFR) gene (677C-T) |
NCBI GTR |
160900 MYOTONIC DYSTROPHY 1; DM1 |
OMIM |
160900 MYOTONIC DYSTROPHY 1; DM1 |
Omim Description |
DM PROTEIN KINASE, INCLUDED |
|
DYSTROPHIA MYOTONICA; DM |
|
DYSTROPHIA MYOTONICA; DMPK |
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MYOTONIC DYSTROPHY |
|
MYOTONIC DYSTROPHY PROTEIN KINASE, INCLUDED; MDPK, INCLUDED |
|
MYOTONIN-PROTEIN KINASE, INCLUDED |
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STEINERT DISEASEDM-KINASE, INCLUDED; DMK, INCLUDED |
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