GM19490
LCL from B-Lymphocyte
Description:
EHLERS-DANLOS SYNDROME, TYPE III
Repository
|
NIGMS Human Genetic Cell Repository
|
Subcollection |
Heritable Diseases |
Class |
Disorders of Connective Tissue, Muscle, and Bone |
Biopsy Source
|
Peripheral vein
|
Cell Type
|
B-Lymphocyte
|
Tissue Type
|
Blood
|
Transformant
|
Epstein-Barr Virus
|
Sample Source
|
LCL from B-Lymphocyte
|
Race
|
White
|
Ethnicity
|
WEST GERMAN
|
Family Member
|
1
|
Relation to Proband
|
proband
|
Confirmation
|
Clinical summary/Case history
|
Species
|
Homo sapiens
|
Common Name
|
Human
|
Remarks
|
|
IDENTIFICATION OF SPECIES OF ORIGIN |
Species of Origin Confirmed by Nucleoside Phosphorylase,Glucose-6-Phosphate Dehydrogenase, and Lactate Dehydrogenase Isoenzyme Electrophoresis |
|
Remarks |
Clinically affected; EDS hypermobility type; velvety, easily bruised, hyperextensible skin; widened atrophic scars; fatty cysts on shin; calcified hematomas on sides of feet; hypermobile joints with chronic joint pain; recurrent sprains of ankles and wrists; recurrent dislocations of digits, ankles and wrists; pes planus; diverticulosis; has had uterine fibroids and endometriomas removed; complains of nausea, vomiting, diarrhea, and abdominal pain; hiatal and right inguinal hernia; frequent respiratory infections; kidney stones; episodes of hypoglycemia; diminished hearing acuity in both ears; mother has bruising problems; paternal half-sister and several maternal uncles also exhibit some EDS symptoms, but no family members have been clinically diagnosed with EDS; same donor as GM19491 Fibroblast |
Split Ratio |
1:4 |
Temperature |
37 C |
Percent CO2 |
5% |
Medium |
Roswell Park Memorial Institute Medium 1640 with 2mM L-glutamine or equivalent |
Serum |
15% fetal bovine serum Not Inactivated |
Substrate |
None specified |
Subcultivation Method |
dilution - add fresh medium |
Supplement |
- |
|
|