| Enzyme | EC Number | Sample Count |
| 1,4-alpha-glucan branching enzyme | 2.4.1.18 | 2 |
| 3-methyl-2-oxobutanoate dehydrogenase | 1.2.4.4 | 16 |
| 6-phosphofructokinase | 2.7.1.11 | 4 |
| acetylcholinesterase | 3.1.1.7 | 1 |
| acyl-CoA dehydrogenase | 1.3.99.3 | 9 |
| adenine phosphoribosyltransferase | 2.4.2.7 | 10 |
| adenosine deaminase | 3.5.4.4 | 56 |
| adenylate kinase | 2.7.4.3 | 1 |
| alanine transaminase | 2.6.1.2 | 1 |
| alkaline phosphatase | 3.1.3.1 | 63 |
| alkylglycerone-phosphate synthase | 2.5.1.26 | 3 |
| alpha-galactosidase | 3.2.1.22 | 7 |
| alpha-glucosidase | 3.2.1.20 | 32 |
| alpha-L-fucosidase | 3.2.1.51 | 12 |
| alpha-mannosidase | 3.2.1.24 | 7 |
| alpha-N-acetylglucosaminidase | 3.2.1.50 | 4 |
| amylo-alpha-1,6-glucosidase | 3.2.1.33 | 9 |
| arginase | 3.5.3.1 | 6 |
| argininosuccinate lyase | 4.3.2.1 | 8 |
| argininosuccinate synthase | 6.3.4.5 | 14 |
| aspartoacylase | 3.5.1.15 | 2 |
| beta-galactosidase | 3.2.1.23 | 10 |
| beta-glucuronidase | 3.2.1.31 | 8 |
| beta-N-acetylhexosaminidase (hexosaminidase A) | 3.2.1.52 | 27 |
| beta-N-acetylhexosaminidase (hexosaminidase B) | 3.2.1.52 | 6 |
| beta-N-acetylhexosaminidase (hexosaminidase) | 3.2.1.52 | 3 |
| biotin--[propionyl-CoA-carboxylase (ATP-hydrolyzing)] ligase | 6.3.4.10 | 2 |
| biotinidase | 3.5.1.12 | 1 |
| carbamoyl-phosphate synthetase | 6.3.4.16 | 2 |
| carbonate dehydratase (carbonic anhydrase I) | 4.2.1.1 | 2 |
| carbonate dehydratase (carbonic anhydrase II) | 4.2.1.1 | 12 |
| ceramidase | 3.5.1.23 | 5 |
| cerebroside-sulfatase | 3.1.6.8 | 12 |
| creatine kinase | 2.7.3.2 | 48 |
| cystathionine gamma-synthase | 2.5.1.48 | 16 |
| exo-alpha-sialidase | 3.2.1.18 | 17 |
| ferrochelatase | 4.99.1.1 | 4 |
| fumarate hydratase | 4.2.1.2 | 1 |
| galactokinase | 2.7.1.6 | 3 |
| galactosylceramidase | 3.2.1.46 | 15 |
| glucose-6-phosphatase | 3.1.3.9 | 10 |
| glucose-6-phosphate 1-dehydrogenase | 1.1.1.49 | 10 |
| glucosylceramidase | 3.2.1.45 | 15 |
| glucuronosyltransferase | 2.4.1.17 | 2 |
| glutaryl-CoA dehydrogenase | 1.3.99.7 | 1 |
| glutathione synthase | 6.3.2.3 | 2 |
| heparan-alpha-glucosaminide N-acetyltransferase | 2.3.1.78 | 2 |
| hyalurononglucosaminidase | 3.2.1.35 | 1 |
| hydroxymethylbilane synthase | 2.5.1.61 | 19 |
| hypoxanthine phosphoribosyltransferase | 2.4.2.8 | 21 |
| iduronate-2-sulfatase | 3.1.6.13 | 9 |
| inositol-polyphosphate 5-phosphatase | 3.1.3.56 | 2 |
| L-iduronidase | 3.2.1.76 | 20 |
| lipoprotein lipase | 3.1.1.34 | 1 |
| long-chain-3-hydroxyacyl-CoA dehydrogenase | 1.1.1.211 | 1 |
| long-chain-acyl-CoA dehydrogenase | 1.3.99.13 | 3 |
| long-chain-alcohol dehydrogenase | 1.1.1.192 | 3 |
| lysine carboxypeptidase | 3.4.17.3 | 1 |
| methionine adenosyltransferase | 2.5.1.6 | 1 |
| methylcrotonyl-CoA carboxylase | 6.4.1.4 | 2 |
| mevalonate kinase | 2.7.1.36 | 2 |
| monophenol monooxygenase | 1.14.18.1 | 2 |
| N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase | 3.5.1.26 | 7 |
| N-acetylgalactosamine-4-sulfatase | 3.1.6.12 | 16 |
| N-acetylgalactosamine-6-sulfatase | 3.1.6.4 | 4 |
| N-sulfoglucosamine sulfohydrolase | 3.10.1.1 | 11 |
| ornithine aminotransferase | 2.6.1.13 | 10 |
| ornithine carbamoyltransferase | 2.1.3.3 | 2 |
| palmitoyl-protein hydrolase | 3.1.2.22 | 13 |
| phophoglycerate kinase | 2.7.2.3 | 2 |
| phosphomannomutase | 5.4.2.8 | 4 |
| phosphorylase | 2.4.1.1 | 2 |
| phosphorylase kinase | 2.7.11.19 | 1 |
| phytanoyl-CoA dioxygenase | 1.14.11.18 | 7 |
| porphobilinogen synthase | 4.2.1.24 | 2 |
| procollagen-lysine 5-dioxygenase | 1.14.11.4 | 4 |
| propionyl-CoA carboxylase | 6.4.1.3 | 9 |
| pyruvate carboxylase | 6.4.1.1 | 3 |
| sphingomyelin phosphodiesterase | 3.1.4.12 | 17 |
| steroid 21-monooxygenase | 1.14.99.10 | 3 |
| sterol esterase | 3.1.1.13 | 9 |
| steryl-sulfatase | 3.1.6.2 | 9 |
| sucrose alpha-glucosidase | 3.2.1.48 | 1 |
| superoxide dismutase | 1.15.1.1 | 1 |
| triacylglycerol lipase | 3.1.1.3 | 4 |
| tripeptidyl-peptidase I | 3.4.14.9 | 1 |
| tyrosine transaminase | 2.6.1.5 | 1 |
| UDP-glucose--hexose-1-phosphate uridylyltransferase | 2.7.7.12 | 24 |
| UDP-N-acetylglucosamine--lysosomal-enzyme N-acetylglucosaminephosphotransferase | 2.7.8.17 | 8 |
| uroporphyrinogen decarboxylase | 4.1.1.37 | 6 |
| uroporphyrinogen-III synthase | 4.2.1.75 | 3 |
| Xaa-His dipeptidase | 3.4.13.3 | 1 |